Familial hypomagnesemia with hypercalciuria and nephrocalcinosis in 2 sisters.

نویسنده

  • Abdulmohsen H Al-Elq
چکیده

Familial hypomagnesemia with hypercalciuria and nephrocalcinosis (FHHNC) is a rare autosomal recessive tubular disorder characterized by excessive renal magnesium and calcium wasting, eventually, progressing to renal failure. It has been recently attributed to a mutation in the Claudin 16 (CLDN 16) gene of the Paracellin-1 (PCLN-1) tight junction protein. Herein, we report 2 sisters with FHHNC. Both sisters presented at an early stage with hypomagnesemia and hypocalcemia. The first patient was initially mislabeled and treated as a case of hypoparathyroidism, while the second patient was diagnosed retrospectively after the diagnosis of her sister. The 2 patients developed end stage renal disease.

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عنوان ژورنال:
  • Saudi medical journal

دوره 29 3  شماره 

صفحات  -

تاریخ انتشار 2008